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Clinical and Experimental Obstetrics & Gynecology  2020, Vol. 47 Issue (3): 434-437    DOI: 10.31083/j.ceog.2020.03.5236
Case Report Previous articles | Next articles
Rare case of bizarre leiomyoma in Mayer-Rokitansky-Küster-Hauser Syndrome
F.Q. Sun1, T. Wang2, *(), X.H. Xu2, C. Han2, J. Jin3
1Department of Gynecology, Minimally Invasive Center, Beijing Obstetrics and Gynecology Hospital, Capital Medical University, Beijing, P.R. China
2Department of Gynecological Oncology, Beijing Obstetrics and Gynecology Hospital, Capital Medical University, Beijing, P.R. China
3Department of Gynecological Endocrinology, Beijing Obstetrics and Gynecology Hospital, Capital Medical University, Beijing, P.R. China
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Abstract  

The authors report a case of leiomyoma that developed from an aplastic uterus in a 38-year-old Chinese female with a typical Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome. She had normal female secondary sexual characteristics, normal external genitalia with discernible vagina, primary amenorrhea, and infertility with asymptomatic a left adnexal mass. Pelvic MRI showed a mass of 3.7 cm in the left pelvis and a mass of 1.5 × 1.4 × 2.6 cm3 in the right pelvis without a normal functioning uterus and vagina between the bladder and rectum. Laparoscopic exploration showed that the bilateral rudimentary uteri located laterally in the pelvis and they had a constant caudal relationship with their paired ovary. The bilateral fallopian tubes and ovaries were normal. A leiomyoma developed from the left rudimentary uteri. Removal of the left leiomyoma, bilateral rudimentary uteri and fallopian tubes was performed with preservation of bilateral ovaries. The histologic diagnosis showed that the bilateral rudimentary uteri had no clear structures of uterine cavity and endometrium, and the bizarre leiomyoma developed from the left rudimentary uterus without necrosis or mitosis.

Key words:  Leiomyoma      Laparoscopic surgery      Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome      MRI     
Submitted:  20 April 2019      Accepted:  20 June 2019      Published:  15 June 2020     
*Corresponding Author(s):  TONG WANG     E-mail:  wangtong_12@126.com

Cite this article: 

F.Q. Sun, T. Wang, X.H. Xu, C. Han, J. Jin. Rare case of bizarre leiomyoma in Mayer-Rokitansky-Küster-Hauser Syndrome. Clinical and Experimental Obstetrics & Gynecology, 2020, 47(3): 434-437.

URL: 

https://ceog.imrpress.com/EN/10.31083/j.ceog.2020.03.5236     OR     https://ceog.imrpress.com/EN/Y2020/V47/I3/434

Figure 1. —  Magnetic resonance imaging scan. (a) T2WI sagittal view: no obvious uterine tissue is seen between the rectum (yellow arrow) and bladder (red arrow). (b) T1WI coronal post-contrast view: green arrow: left leiomyoma, blue arrow: right rudimentary uterus, and red arrow: bladder.

Figure 2. —  Laparoscopic view: green arrow: left leiomyoma, blue arrow: right rudimentary uterus, white arrow: bilateral fallopian tube, red arrow: left ovary with the follicular development, and black arrow: right ovary.

Figure 3. —  Cut sections of left leiomyoma, bilateral rudimentary uteri and fallopian tubes.

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